The so-called striated muscle hamartoma is a hamartoma of cutaneous adnexa and mesenchyme, but not of striated muscle.

Sir, Striatedmusclehamartomaorrhabdomyomatousmesenchymal hamartoma is a rare benign papillomatous lesion occurring on the face and neck that is usually present from birth. It has been reported indi¡erent races inmales and females.Histopathologically, the lesion consists of a core of ¢broadipous tissue covered by a normal epidermis and containing abundant hair follicles, sebaceous and eccrine glands, nerve ¢bres, blood vessels, and mature striatedmuscle, in the formof individual ¢bres penetrating into the dermis and arranged perpendicularly to the epidermis. Some patients with striated muscle hamartoma have Delleman's syndrome, a recentlydescribed syndrome characterized by ocular cysts, cerebral malformations, focal cutaneous hypoplasia and accessory skin appendages (1). The presence of striatedmusclehasbeen considered itsmost characteristic histopathologic ¢nding, and therefore the name ``striated muscle hamartoma'' has been the most frequent denomination for this lesion. In our opinion, striated muscle is a normal component of the dermis in some cutaneous areas of the face, the same areas where this hamartoma is located.For this reason,webelieve that ``striated muscle hamartoma'' is a misnomer, and that hamartoma of adnexa and mesenchyme is the most appropriate denomination for this entity. We present herein an additional example of this hamartoma.